2023-06-262023-06-262023-03-09CARDOSO, Caroline de Morais. Elaboração de uma cartilha com orientações nutricionais para pacientes diagnosticados com fenilcetonúria. Orientador: Luiz Carlos Santana da Silva. 2023. 34 f. Trabalho de Curso (Bacharelado em Nutrição) - Faculdade de Nutrição, Instituto de Ciências da Saúde, Universidade Federal do Pará, Belém, 2023. Disponível em: https://bdm.ufpa.br/handle/prefix/5785. Acesso em:.https://bdm.ufpa.br/handle/prefix/5785Introduction: Phenylketonuria (PKU) is a inborn error of amino acid metabolism in which there is reduced activity of the enzyme that converts phenylalanine into tyrosine. The diagnosis is made by the neonatal screening test and its treatment must be started as soon as possible and maintained throughout life. The main treatment is a low phenylalanine diet, following the patient's tolerance; therefore the objective of the present work is to develop a booklet with nutritional guidelines for patients diagnosed with PKU, to be used as support in their treatment. Methodology: This is a descriptive study with a qualitative approach through an Integrative Literature Review, carried out from August to November 2022. Articles from the Lilacs, Pubmed, Google Scholar and Scielo were selected, in addition to manuals from the Ministério da Saúde (MS), from 2017 to 2022 based on the following keywords: health education, diet therapy in PKU, breastfeeding in PKU and child health. Articles not available in full, not related to the topic, theses and dissertations were excluded. The study was carried out in two stages, the survey of scientific information and the construction of the booklet. Results: Three articles and Clinical Practice Guidelines Phenylketonuria were used in the construction of the booklet. A digital booklet was then prepared, with the topics: Introduction, Food groups, Breastfeeding, Allowed Foods, Moderate Consumption Foods and Prohibited Foods. Conclusion: The booklet is an educational technology that can assists in the nutritional guidance of children with PKU.Acesso AbertoFenilcetonúriaDietoterapiaCartilhaEducação em saúdePhenylketonuriaDiet therapyBookletHealth educationCNPQ::CIENCIAS DA SAUDE::NUTRIÇÃOTrabalho de Curso - Graduação - Monografia